Alpha-L-iduronidase deficiency in a cat: a model of mucopolysaccharidosis I. [electronic resource]
Producer: 19800226Description: 1294-7 p. digitalISSN:- 0031-3998
- Animals
- Cat Diseases -- diagnosis
- Cats
- Cells, Cultured
- Disease Models, Animal
- Fibroblasts -- enzymology
- Glycosaminoglycans -- urine
- Glycoside Hydrolases -- deficiency
- Humans
- Iduronidase -- deficiency
- Leukocytes -- ultrastructure
- Lysosomes -- enzymology
- Male
- Mucopolysaccharidosis I -- diagnosis
- Neurons -- ultrastructure
- Skin -- pathology
- Spinal Cord -- ultrastructure
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Publication Type: Journal Article; Research Support, U.S. Gov't, P.H.S.
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