Effect of idebenone on cardiomyopathy in Friedreich's ataxia: a preliminary study. [electronic resource]
Producer: 19990902Description: 477-9 p. digitalISSN:- 0140-6736
- Adult
- Antioxidants -- adverse effects
- Benzoquinones -- adverse effects
- Cardiac Volume -- drug effects
- Cardiomyopathies -- drug therapy
- Child
- Electron Transport Complex II
- Female
- Friedreich Ataxia -- drug therapy
- Humans
- Iron Chelating Agents -- adverse effects
- Male
- Multienzyme Complexes -- metabolism
- Myocardium -- pathology
- Oxidoreductases -- metabolism
- Succinate Dehydrogenase -- metabolism
- Ubiquinone -- analogs & derivatives
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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