Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocytopenic purpura.

Furlan, M

Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocytopenic purpura. [electronic resource] - Blood May 1997 - 3097-103 p. digital

Publication Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't

0006-4971


ADAM Proteins
ADAMTS13 Protein
Adult
Anemia, Hemolytic--blood
Disulfides
Female
Humans
Macromolecular Substances
Male
Metalloendopeptidases--blood
Middle Aged
Nuclear Family
Protease Inhibitors--pharmacology
Purpura, Thrombotic Thrombocytopenic--blood
Reference Values
von Willebrand Factor--metabolism