Glucosylceramide and glucosylsphingosine metabolism in cultured fibroblasts deficient in acid beta-glucosidase activity.

Sasagasako, N

Glucosylceramide and glucosylsphingosine metabolism in cultured fibroblasts deficient in acid beta-glucosidase activity. [electronic resource] - Journal of biochemistry Jan 1994 - 113-9 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0021-924X

10.1093/oxfordjournals.jbchem.a124284 doi


Cells, Cultured
Fibroblasts--enzymology
Gaucher Disease--metabolism
Glucosylceramidase--deficiency
Glucosylceramides--metabolism
Humans
Psychosine--analogs & derivatives