The Twitcher mouse: an enzymatically authentic model of human globoid cell leukodystrophy (Krabbe disease).
Kobayashi, T
The Twitcher mouse: an enzymatically authentic model of human globoid cell leukodystrophy (Krabbe disease). [electronic resource] - Brain research Dec 1980 - 479-83 p. digital
Publication Type: Journal Article; Research Support, U.S. Gov't, P.H.S.
0006-8993
10.1016/0006-8993(80)90159-6 doi
Animals
Disease Models, Animal
Galactosidases--metabolism
Galactosylceramidase--deficiency
Lactosylceramides--metabolism
Leukodystrophy, Globoid Cell--enzymology
Lysosomes--enzymology
Mice
Mice, Neurologic Mutants
The Twitcher mouse: an enzymatically authentic model of human globoid cell leukodystrophy (Krabbe disease). [electronic resource] - Brain research Dec 1980 - 479-83 p. digital
Publication Type: Journal Article; Research Support, U.S. Gov't, P.H.S.
0006-8993
10.1016/0006-8993(80)90159-6 doi
Animals
Disease Models, Animal
Galactosidases--metabolism
Galactosylceramidase--deficiency
Lactosylceramides--metabolism
Leukodystrophy, Globoid Cell--enzymology
Lysosomes--enzymology
Mice
Mice, Neurologic Mutants