Search for the biochemical basis of biotin dependent multiple carboxylase deficiencies: determination of biotin activation in cultured fibroblasts.

Zamboni, M

Search for the biochemical basis of biotin dependent multiple carboxylase deficiencies: determination of biotin activation in cultured fibroblasts. [electronic resource] - Clinica chimica acta; international journal of clinical chemistry Jul 1982 - 241-8 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0009-8981

10.1016/0009-8981(82)90283-2 doi


Adenosine Monophosphate--analogs & derivatives
Biotin--analogs & derivatives
Carbon-Nitrogen Ligases
Carboxy-Lyases--deficiency
Cells, Cultured
Fibroblasts--drug effects
Humans
Kinetics
Ligases--metabolism