Possible metabolic basis for the different immunodeficient states associated with genetic deficiencies of adenosine deaminase and purine nucleoside phosphorylase.

Carson, D A

Possible metabolic basis for the different immunodeficient states associated with genetic deficiencies of adenosine deaminase and purine nucleoside phosphorylase. [electronic resource] - Proceedings of the National Academy of Sciences of the United States of America Jun 1982 - 3848-52 p. digital

Publication Type: Journal Article; Research Support, U.S. Gov't, P.H.S.

0027-8424

10.1073/pnas.79.12.3848 doi


Adenosine--analogs & derivatives
Adenosine Deaminase--deficiency
Adenosine Deaminase Inhibitors
Cell Division
Deoxyadenosines--toxicity
Deoxycytidine--toxicity
Deoxyguanosine--toxicity
Humans
Lymphocytes--metabolism
Models, Biological
Nucleoside Deaminases--deficiency
Pentosyltransferases--deficiency
Purine-Nucleoside Phosphorylase--deficiency