Decreased ganglioside neuraminidase activity in fibroblasts from mucopolysaccharidosis patients. Inhibition of the activity in vitro by sulfated glycosaminoglycans and other compounds.
Baumkötter, J
Decreased ganglioside neuraminidase activity in fibroblasts from mucopolysaccharidosis patients. Inhibition of the activity in vitro by sulfated glycosaminoglycans and other compounds. [electronic resource] - Biochimica et biophysica acta Dec 1983 - 163-70 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
0006-3002
10.1016/0304-4165(83)90225-8 doi
Gangliosides--metabolism
Glycosaminoglycans--pharmacology
Humans
Mucopolysaccharidoses--enzymology
Neuraminidase--antagonists & inhibitors
Osmolar Concentration
Decreased ganglioside neuraminidase activity in fibroblasts from mucopolysaccharidosis patients. Inhibition of the activity in vitro by sulfated glycosaminoglycans and other compounds. [electronic resource] - Biochimica et biophysica acta Dec 1983 - 163-70 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
0006-3002
10.1016/0304-4165(83)90225-8 doi
Gangliosides--metabolism
Glycosaminoglycans--pharmacology
Humans
Mucopolysaccharidoses--enzymology
Neuraminidase--antagonists & inhibitors
Osmolar Concentration