Clinically-approved CFTR modulators rescue Nrf2 dysfunction in cystic fibrosis airway epithelia.

Borcherding, Dana C

Clinically-approved CFTR modulators rescue Nrf2 dysfunction in cystic fibrosis airway epithelia. [electronic resource] - The Journal of clinical investigation 05 2019 - 3448-3463 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural

1558-8238

10.1172/JCI96273 doi


Active Transport, Cell Nucleus--genetics
Animals
Cell Line
Cell Nucleus--genetics
Cystic Fibrosis--genetics
Cystic Fibrosis Transmembrane Conductance Regulator--genetics
Epithelial Cells--metabolism
Humans
Mice
Mice, Transgenic
Mutation
NF-E2-Related Factor 2--genetics
Phosphorylation--genetics
Respiratory Mucosa--metabolism