A Wars2 Mutant Mouse Model Displays OXPHOS Deficiencies and Activation of Tissue-Specific Stress Response Pathways.
Agnew, Thomas
A Wars2 Mutant Mouse Model Displays OXPHOS Deficiencies and Activation of Tissue-Specific Stress Response Pathways. [electronic resource] - Cell reports 12 2018 - 3315-3328.e6 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
2211-1247
10.1016/j.celrep.2018.11.080 doi
Adipose Tissue, Brown--pathology
Adipose Tissue, White--pathology
Adiposity
Alleles
Alternative Splicing--genetics
Animals
Base Sequence
Body Weight
Brain--pathology
Cardiomyopathy, Hypertrophic--blood
Disease Models, Animal
Electron Transport
Evoked Potentials, Auditory, Brain Stem
Exons--genetics
Fibroblast Growth Factors--blood
Fibroblasts--metabolism
Hearing Loss--blood
Mice
Mice, Mutant Strains
Muscle, Skeletal--metabolism
Mutation--genetics
Organ Specificity
Organelle Biogenesis
Oxidative Phosphorylation
Stress, Physiological
Tryptophan-tRNA Ligase--genetics
Up-Regulation
A Wars2 Mutant Mouse Model Displays OXPHOS Deficiencies and Activation of Tissue-Specific Stress Response Pathways. [electronic resource] - Cell reports 12 2018 - 3315-3328.e6 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
2211-1247
10.1016/j.celrep.2018.11.080 doi
Adipose Tissue, Brown--pathology
Adipose Tissue, White--pathology
Adiposity
Alleles
Alternative Splicing--genetics
Animals
Base Sequence
Body Weight
Brain--pathology
Cardiomyopathy, Hypertrophic--blood
Disease Models, Animal
Electron Transport
Evoked Potentials, Auditory, Brain Stem
Exons--genetics
Fibroblast Growth Factors--blood
Fibroblasts--metabolism
Hearing Loss--blood
Mice
Mice, Mutant Strains
Muscle, Skeletal--metabolism
Mutation--genetics
Organ Specificity
Organelle Biogenesis
Oxidative Phosphorylation
Stress, Physiological
Tryptophan-tRNA Ligase--genetics
Up-Regulation