Everolimus rescues multiple cellular defects in laminopathy-patient fibroblasts.
DuBose, Amanda J
Everolimus rescues multiple cellular defects in laminopathy-patient fibroblasts. [electronic resource] - Proceedings of the National Academy of Sciences of the United States of America 04 2018 - 4206-4211 p. digital
Publication Type: Journal Article
1091-6490
10.1073/pnas.1802811115 doi
Biomarkers
Cell Division--drug effects
Cell Line
Cell Nucleus--drug effects
Cellular Senescence--drug effects
Everolimus--pharmacology
Fibroblasts--drug effects
Humans
Lamin Type A--deficiency
Muscular Dystrophy, Emery-Dreifuss--genetics
Mutation
Phosphorylation--drug effects
Progeria--genetics
Protein Processing, Post-Translational--drug effects
Ribosomal Protein S6--metabolism
TOR Serine-Threonine Kinases--antagonists & inhibitors
Werner Syndrome--genetics
Everolimus rescues multiple cellular defects in laminopathy-patient fibroblasts. [electronic resource] - Proceedings of the National Academy of Sciences of the United States of America 04 2018 - 4206-4211 p. digital
Publication Type: Journal Article
1091-6490
10.1073/pnas.1802811115 doi
Biomarkers
Cell Division--drug effects
Cell Line
Cell Nucleus--drug effects
Cellular Senescence--drug effects
Everolimus--pharmacology
Fibroblasts--drug effects
Humans
Lamin Type A--deficiency
Muscular Dystrophy, Emery-Dreifuss--genetics
Mutation
Phosphorylation--drug effects
Progeria--genetics
Protein Processing, Post-Translational--drug effects
Ribosomal Protein S6--metabolism
TOR Serine-Threonine Kinases--antagonists & inhibitors
Werner Syndrome--genetics