Short chain acyl-coenzyme A dehydrogenase (SCAD) deficiency. Immunochemical demonstration of molecular heterogeneity due to variant SCAD with differing stability.

Naito, E

Short chain acyl-coenzyme A dehydrogenase (SCAD) deficiency. Immunochemical demonstration of molecular heterogeneity due to variant SCAD with differing stability. [electronic resource] - The Journal of clinical investigation Nov 1989 - 1671-4 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.

0021-9738

10.1172/JCI114346 doi


Acyl-CoA Dehydrogenases--genetics
Animals
Butyryl-CoA Dehydrogenase
Cell Line
Fibroblasts--enzymology
Genetic Variation
Humans
Immunoblotting
Liver--enzymology
Methionine--metabolism
Mitochondria--metabolism
Protein Precursors--metabolism
Rats