Oxidative stress and mitochondrial dynamics malfunction are linked in Pelizaeus-Merzbacher disease.

Ruiz, Montserrat

Oxidative stress and mitochondrial dynamics malfunction are linked in Pelizaeus-Merzbacher disease. [electronic resource] - Brain pathology (Zurich, Switzerland) 09 2018 - 611-630 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1750-3639

10.1111/bpa.12571 doi


Animals
Cells, Cultured
Child
Child, Preschool
DNA, Mitochondrial
Fibroblasts--metabolism
Glutamic Acid--metabolism
Humans
Infant
Male
Mice, Inbred C57BL
Mice, Transgenic
Mitochondria--metabolism
Mitochondrial Dynamics
Mitochondrial Proteins--metabolism
Myelin Proteolipid Protein--genetics
Oxidative Stress
Pelizaeus-Merzbacher Disease--metabolism
RNA, Messenger--metabolism
Spinal Cord--metabolism