Patient iPSC-Derived Neurons for Disease Modeling of Frontotemporal Dementia with Mutation in CHMP2B.

Zhang, Yu

Patient iPSC-Derived Neurons for Disease Modeling of Frontotemporal Dementia with Mutation in CHMP2B. [electronic resource] - Stem cell reports 03 2017 - 648-658 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

2213-6711

10.1016/j.stemcr.2017.01.012 doi


Cell Differentiation
Cellular Reprogramming
Endosomal Sorting Complexes Required for Transport--genetics
Endosomes--metabolism
Fibroblasts--cytology
Frontotemporal Dementia--genetics
Gene Expression Profiling
Humans
Induced Pluripotent Stem Cells--cytology
Iron--metabolism
Mitochondria--genetics
Mutation
Neurons--cytology
Oxidative Stress--genetics
Transcriptome