Extensive pulmonary sarcoid reaction in a patient with BMPR-2 associated idiopathic pulmonary arterial hypertension.

Braam, Evelien A J E

Extensive pulmonary sarcoid reaction in a patient with BMPR-2 associated idiopathic pulmonary arterial hypertension. [electronic resource] - Sarcoidosis, vasculitis, and diffuse lung diseases : official journal of WASOG Aug 2016 - 182-5 p. digital

Publication Type: Case Reports; Journal Article

2532-179X


Adult
Biopsy
Bone Morphogenetic Protein Receptors, Type II--genetics
Familial Primary Pulmonary Hypertension--complications
Female
Genetic Predisposition to Disease
Humans
Lung Transplantation
Mutation
Sarcoidosis, Pulmonary--diagnosis