C9orf72 BAC Transgenic Mice Display Typical Pathologic Features of ALS/FTD.

O'Rourke, Jacqueline G

C9orf72 BAC Transgenic Mice Display Typical Pathologic Features of ALS/FTD. [electronic resource] - Neuron Dec 2015 - 892-901 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, Non-P.H.S.

1097-4199

10.1016/j.neuron.2015.10.027 doi


Age Factors
Amyotrophic Lateral Sclerosis--genetics
Animals
Brain--metabolism
C9orf72 Protein
Cells, Cultured
Chromosomes, Artificial, Bacterial--genetics
DNA Repeat Expansion--genetics
Disease Models, Animal
Frontotemporal Dementia--genetics
Glutamic Acid--pharmacology
Humans
Mice
Mice, Transgenic
Motor Activity--genetics
Muscle Strength--genetics
Neuromuscular Junction--genetics
Neurons--drug effects
Proteins--genetics
Psychomotor Performance--physiology
Spinal Cord--metabolism