Circadian profiling in two mouse models of lysosomal storage disorders; Niemann Pick type-C and Sandhoff disease.

Richardson, Katie

Circadian profiling in two mouse models of lysosomal storage disorders; Niemann Pick type-C and Sandhoff disease. [electronic resource] - Behavioural brain research Jan 2016 - 213-23 p. digital

Publication Type: Comparative Study; Journal Article; Research Support, Non-U.S. Gov't

1872-7549

10.1016/j.bbr.2015.10.021 doi


Actigraphy
Animals
CLOCK Proteins--metabolism
Cholesterol--metabolism
Circadian Rhythm--physiology
Disease Models, Animal
Fluorescent Antibody Technique
Intracellular Signaling Peptides and Proteins
Mice, Inbred BALB C
Mice, Knockout
Motor Activity--physiology
Niemann-Pick C1 Protein
Niemann-Pick Disease, Type C--pathology
Photoperiod
Proteins--genetics
Retina--metabolism
Rod Opsins--metabolism
Sandhoff Disease--pathology
Suprachiasmatic Nucleus--pathology
Transcription Factor Brn-3A--metabolism
beta-N-Acetylhexosaminidases--genetics