Altered hepatic sulfur metabolism in cystathionine β-synthase-deficient homocystinuria: regulatory role of taurine on competing cysteine oxidation pathways.

Jiang, Hua

Altered hepatic sulfur metabolism in cystathionine β-synthase-deficient homocystinuria: regulatory role of taurine on competing cysteine oxidation pathways. [electronic resource] - FASEB journal : official publication of the Federation of American Societies for Experimental Biology Sep 2014 - 4044-54 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1530-6860

10.1096/fj.14-253633 doi


Animals
Blotting, Western
Carboxy-Lyases--genetics
Cystathionine beta-Synthase--physiology
Cysteine--chemistry
Cysteine Dioxygenase--genetics
Dietary Supplements
Female
Homocystinuria--drug therapy
Humans
Liver--drug effects
Male
Methionine--metabolism
Mice
Mice, Inbred C57BL
Mice, Knockout
Mice, Transgenic
Oxidation-Reduction
RNA, Messenger--genetics
Real-Time Polymerase Chain Reaction
Reverse Transcriptase Polymerase Chain Reaction
Sulfur--metabolism
Taurine--pharmacology