Dysregulation of ubiquitin homeostasis and β-catenin signaling promote spinal muscular atrophy.
Wishart, Thomas M
Dysregulation of ubiquitin homeostasis and β-catenin signaling promote spinal muscular atrophy. [electronic resource] - The Journal of clinical investigation Apr 2014 - 1821-34 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
1558-8238
10.1172/JCI71318 doi
Alternative Splicing
Animals
Disease Models, Animal
Drosophila
Homeostasis
Humans
Isoenzymes--genetics
Mice
Mice, Knockout
Mice, Mutant Strains
Mice, Transgenic
Muscle, Skeletal--metabolism
Muscular Atrophy, Spinal--etiology
RNA, Messenger--genetics
Rats
Signal Transduction
Spinal Cord--metabolism
Survival of Motor Neuron 1 Protein--genetics
Ubiquitin--metabolism
Ubiquitin-Activating Enzymes--antagonists & inhibitors
Zebrafish
beta Catenin--metabolism
Dysregulation of ubiquitin homeostasis and β-catenin signaling promote spinal muscular atrophy. [electronic resource] - The Journal of clinical investigation Apr 2014 - 1821-34 p. digital
Publication Type: Journal Article; Research Support, Non-U.S. Gov't
1558-8238
10.1172/JCI71318 doi
Alternative Splicing
Animals
Disease Models, Animal
Drosophila
Homeostasis
Humans
Isoenzymes--genetics
Mice
Mice, Knockout
Mice, Mutant Strains
Mice, Transgenic
Muscle, Skeletal--metabolism
Muscular Atrophy, Spinal--etiology
RNA, Messenger--genetics
Rats
Signal Transduction
Spinal Cord--metabolism
Survival of Motor Neuron 1 Protein--genetics
Ubiquitin--metabolism
Ubiquitin-Activating Enzymes--antagonists & inhibitors
Zebrafish
beta Catenin--metabolism