Histone deacetylase 6-mediated selective autophagy regulates COPD-associated cilia dysfunction.

Lam, Hilaire C

Histone deacetylase 6-mediated selective autophagy regulates COPD-associated cilia dysfunction. [electronic resource] - The Journal of clinical investigation Dec 2013 - 5212-30 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1558-8238

10.1172/JCI69636 doi


Animals
Apoptosis Regulatory Proteins--deficiency
Autophagy--physiology
Beclin-1
Cells, Cultured
Cilia--physiology
Cytosol--enzymology
Epithelial Cells--ultrastructure
Female
Histone Deacetylase 6
Histone Deacetylase Inhibitors--pharmacology
Histone Deacetylases--physiology
Humans
Male
Mice
Mice, Inbred C57BL
Mice, Knockout
Microscopy, Electron, Scanning
Microtubule-Associated Proteins--deficiency
Mucus
NF-E2-Related Factor 2--deficiency
Phenotype
Phenylbutyrates--pharmacology
Proteasome Endopeptidase Complex--metabolism
Protein Processing, Post-Translational
Pulmonary Disease, Chronic Obstructive--enzymology
Sirtuin 1--deficiency
Tobacco Products
Tobacco Smoke Pollution--adverse effects
Trachea--cytology
Ubiquitination