Spinal muscular atrophy astrocytes exhibit abnormal calcium regulation and reduced growth factor production.

McGivern, Jered V

Spinal muscular atrophy astrocytes exhibit abnormal calcium regulation and reduced growth factor production. [electronic resource] - Glia Sep 2013 - 1418-1428 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1098-1136

10.1002/glia.22522 doi


Adenosine Triphosphate--pharmacology
Age Factors
Aldehyde Dehydrogenase--metabolism
Analysis of Variance
Animals
Animals, Newborn
Astrocytes--drug effects
Calcium--metabolism
Cell Line, Transformed
Choline O-Acetyltransferase--metabolism
Disease Models, Animal
Gene Expression Regulation, Developmental--genetics
Glial Cell Line-Derived Neurotrophic Factor--metabolism
Glial Fibrillary Acidic Protein--metabolism
Humans
Mice
Mice, Transgenic
Muscular Atrophy, Spinal--genetics
Mutation--genetics
Nestin--metabolism
Oxidoreductases Acting on CH-NH Group Donors
Pluripotent Stem Cells--metabolism
Receptors, Purinergic P2Y2--metabolism
S100 Proteins--metabolism
Spinal Cord--cytology
Survival of Motor Neuron 1 Protein--genetics
Survival of Motor Neuron 2 Protein--metabolism