Age-dependent chloride channel expression in skeletal muscle fibres of normal and HSA(LR) myotonic mice.

DiFranco, Marino

Age-dependent chloride channel expression in skeletal muscle fibres of normal and HSA(LR) myotonic mice. [electronic resource] - The Journal of physiology Mar 2013 - 1347-71 p. digital

Publication Type: Comparative Study; Journal Article; Research Support, N.I.H., Extramural

1469-7793

10.1113/jphysiol.2012.246546 doi


Actinin--genetics
Age Factors
Aging--genetics
Animals
Chloride Channels--genetics
Disease Models, Animal
Electric Impedance
Genotype
Humans
Membrane Potentials
Mice
Mice, Transgenic
Mosaicism
Muscle Fibers, Skeletal--metabolism
Myotonic Dystrophy--genetics
Patch-Clamp Techniques
Phenotype
Sarcolemma--metabolism
Time Factors
Voltage-Sensitive Dye Imaging