Adaptation of respiratory chain biogenesis to cytochrome c oxidase deficiency caused by SURF1 gene mutations.

Kovářová, Nikola

Adaptation of respiratory chain biogenesis to cytochrome c oxidase deficiency caused by SURF1 gene mutations. [electronic resource] - Biochimica et biophysica acta Jul 2012 - 1114-24 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0006-3002

10.1016/j.bbadis.2012.03.007 doi


Cell Extracts
Cell Line
Cyclooxygenase 1--genetics
Cyclooxygenase 2--genetics
Cytochrome-c Oxidase Deficiency--genetics
Electron Transport--physiology
Electron Transport Complex I--genetics
Electron Transport Complex III--genetics
Electron Transport Complex IV--genetics
Female
Fibroblasts--cytology
Humans
Leigh Disease--genetics
Male
Membrane Proteins--genetics
Mitochondria--genetics
Mitochondrial Proteins--genetics
Mutation--genetics
Oxidative Phosphorylation
Protein Subunits--genetics