Voltage-gated ion channel dysfunction precedes cardiomyopathy development in the dystrophic heart.

Koenig, Xaver

Voltage-gated ion channel dysfunction precedes cardiomyopathy development in the dystrophic heart. [electronic resource] - PloS one 2011 - e20300 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1932-6203

10.1371/journal.pone.0020300 doi


Action Potentials--physiology
Animals
Animals, Newborn
Barium--metabolism
Calcium Channels, L-Type--metabolism
Cardiomyopathies--pathology
Cells, Cultured
Dystrophin--genetics
Electrocardiography
Humans
Mice
Mice, Inbred C57BL
Mice, Inbred mdx
Muscular Dystrophy, Duchenne--genetics
Mutation
Myocytes, Cardiac--cytology
Patch-Clamp Techniques
Sodium--metabolism
Sodium Channels--metabolism
Utrophin--deficiency