Cardiac defects contribute to the pathology of spinal muscular atrophy models.

Shababi, Monir

Cardiac defects contribute to the pathology of spinal muscular atrophy models. [electronic resource] - Human molecular genetics Oct 2010 - 4059-71 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1460-2083

10.1093/hmg/ddq329 doi


Animals
Disease Models, Animal
Fibrosis
Gene Expression
Heart Defects, Congenital--genetics
Heart Septum--embryology
Humans
Hypoplastic Left Heart Syndrome--genetics
Mice
Motor Neurons--metabolism
Muscular Atrophy--genetics
Muscular Atrophy, Spinal--genetics
Myocardium--metabolism
Nerve Tissue Proteins--genetics
Oxidative Stress
Survival of Motor Neuron 1 Protein--genetics
Survival of Motor Neuron 2 Protein--genetics
Ventricular Remodeling