A chemical corrector modifies the channel function of F508del-CFTR.

Kim Chiaw, Patrick

A chemical corrector modifies the channel function of F508del-CFTR. [electronic resource] - Molecular pharmacology Sep 2010 - 411-8 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1521-0111

10.1124/mol.110.065862 doi


Animals
Cricetinae
Cystic Fibrosis--genetics
Cystic Fibrosis Transmembrane Conductance Regulator--genetics
Endoplasmic Reticulum--genetics
Mutation
Phenylalanine--genetics
Piperazines
Protein Transport--genetics
Quinazolines--metabolism
Sequence Deletion