Effect of gene dosage on single-cell hippocampal electrophysiology in a murine model of SSADH deficiency (gamma-hydroxybutyric aciduria).

Dósa, Zita

Effect of gene dosage on single-cell hippocampal electrophysiology in a murine model of SSADH deficiency (gamma-hydroxybutyric aciduria). [electronic resource] - Epilepsy research Jun 2010 - 39-46 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1872-6844

10.1016/j.eplepsyres.2010.03.005 doi


Animals
Animals, Newborn
Biophysics
Disease Models, Animal
Dose-Response Relationship, Drug
Electric Stimulation--methods
Female
GABA Antagonists--pharmacology
Gene Dosage--genetics
Hippocampus--pathology
Humans
In Vitro Techniques
Linear Models
Lysine--analogs & derivatives
Male
Membrane Potentials--drug effects
Mice
Mice, Knockout
Neurons--classification
Patch-Clamp Techniques--methods
Pyridazines--pharmacology
Seizures--genetics
Succinate-Semialdehyde Dehydrogenase--deficiency
gamma-Aminobutyric Acid--metabolism