Increased life span and correction of metabolic defects in murine mucopolysaccharidosis type VII after syngeneic bone marrow transplantation.
Birkenmeier, E H
Increased life span and correction of metabolic defects in murine mucopolysaccharidosis type VII after syngeneic bone marrow transplantation. [electronic resource] - Blood Dec 1991 - 3081-92 p. digital
Publication Type: Journal Article; Research Support, U.S. Gov't, P.H.S.
0006-4971
Animals
Bone Marrow Transplantation
Dose-Response Relationship, Radiation
Glucuronidase--metabolism
Glycosaminoglycans--metabolism
Granulocytes--ultrastructure
Lysosomes--enzymology
Mice
Mice, Mutant Strains
Microscopy, Electron
Mucopolysaccharidoses--metabolism
Survival Analysis
Whole-Body Irradiation
Increased life span and correction of metabolic defects in murine mucopolysaccharidosis type VII after syngeneic bone marrow transplantation. [electronic resource] - Blood Dec 1991 - 3081-92 p. digital
Publication Type: Journal Article; Research Support, U.S. Gov't, P.H.S.
0006-4971
Animals
Bone Marrow Transplantation
Dose-Response Relationship, Radiation
Glucuronidase--metabolism
Glycosaminoglycans--metabolism
Granulocytes--ultrastructure
Lysosomes--enzymology
Mice
Mice, Mutant Strains
Microscopy, Electron
Mucopolysaccharidoses--metabolism
Survival Analysis
Whole-Body Irradiation