A potential role for muscle in glucose homeostasis: in vivo kinetic studies in glycogen storage disease type 1a and fructose-1,6-bisphosphatase deficiency.

Huidekoper, Hidde H

A potential role for muscle in glucose homeostasis: in vivo kinetic studies in glycogen storage disease type 1a and fructose-1,6-bisphosphatase deficiency. [electronic resource] - Journal of inherited metabolic disease Feb 2010 - 25-31 p. digital

Publication Type: Case Reports; Journal Article

1573-2665

10.1007/s10545-009-9030-9 doi


Adolescent
Blood Glucose--metabolism
Female
Fructose-1,6-Diphosphatase Deficiency--genetics
Gluconeogenesis
Glucose--metabolism
Glycogen Storage Disease Type I--genetics
Glycogenolysis
Homeostasis
Humans
Hypoglycemia--genetics
Kinetics
Liver--metabolism
Male
Muscles--metabolism