Mouse models for nuclear DNA-encoded mitochondrial complex I deficiency.

Koene, Saskia

Mouse models for nuclear DNA-encoded mitochondrial complex I deficiency. [electronic resource] - Journal of inherited metabolic disease Apr 2011 - 293-307 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Review

1573-2665

10.1007/s10545-009-9005-x doi


Animals
Cell Nucleus--genetics
DNA--genetics
DNA, Mitochondrial--genetics
Disease Models, Animal
Electron Transport Complex I--deficiency
Humans
Mice
Mice, Knockout
Mitochondrial Diseases--genetics
Models, Biological
Oxidative Phosphorylation
Reactive Oxygen Species
Treatment Outcome