Neuroprotective function of cellular prion protein in a mouse model of amyotrophic lateral sclerosis.

Steinacker, Petra

Neuroprotective function of cellular prion protein in a mouse model of amyotrophic lateral sclerosis. [electronic resource] - The American journal of pathology Mar 2010 - 1409-20 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1525-2191

10.2353/ajpath.2010.090355 doi


Amyotrophic Lateral Sclerosis--enzymology
Animals
Brain--enzymology
Breeding
Cell Count
DNA--metabolism
Disease Models, Animal
Disease Progression
Enzyme Activation
Female
Glial Fibrillary Acidic Protein--metabolism
Humans
Male
Mice
Mice, Transgenic
Mitogen-Activated Protein Kinase 1--metabolism
Motor Neurons--pathology
Neuroprotective Agents--metabolism
Prion Proteins
Prions--metabolism
Spinal Cord--enzymology
Superoxide Dismutase--genetics
Superoxide Dismutase-1
Survival Analysis
Transgenes--genetics
Vacuoles--metabolism