Reduced central tolerance in Omenn syndrome leads to immature self-reactive oligoclonal T cells.

Somech, Raz

Reduced central tolerance in Omenn syndrome leads to immature self-reactive oligoclonal T cells. [electronic resource] - The Journal of allergy and clinical immunology Oct 2009 - 793-800 p. digital

Publication Type: Journal Article

1097-6825

10.1016/j.jaci.2009.06.048 doi


Autoimmunity--genetics
CD4-Positive T-Lymphocytes--immunology
Clone Cells--immunology
Cytokines--immunology
Down-Regulation--genetics
Female
Forkhead Transcription Factors--immunology
Gene Expression
Gene Rearrangement, T-Lymphocyte
Humans
Immune Tolerance
Male
Receptors, Antigen, T-Cell--genetics
Severe Combined Immunodeficiency--genetics
T-Lymphocytes, Regulatory--immunology
Transcription Factors--immunology
Up-Regulation--genetics
AIRE Protein