Limitations in a frataxin knockdown cell model for Friedreich ataxia in a high-throughput drug screen.

Calmels, Nadège

Limitations in a frataxin knockdown cell model for Friedreich ataxia in a high-throughput drug screen. [electronic resource] - BMC neurology Aug 2009 - 46 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1471-2377

10.1186/1471-2377-9-46 doi


Animals
Blotting, Western
Cell Line--cytology
Cell Proliferation
Cells, Cultured
Drug Evaluation, Preclinical
Friedreich Ataxia--drug therapy
Gene Knockdown Techniques
Iron-Binding Proteins--genetics
Iron-Sulfur Proteins--genetics
Mice
Mitochondrial Proteins--genetics
Reverse Transcriptase Polymerase Chain Reaction
Frataxin