PGC-1alpha/beta induced expression partially compensates for respiratory chain defects in cells from patients with mitochondrial disorders.

Srivastava, Sarika

PGC-1alpha/beta induced expression partially compensates for respiratory chain defects in cells from patients with mitochondrial disorders. [electronic resource] - Human molecular genetics May 2009 - 1805-12 p. digital

Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't

1460-2083

10.1093/hmg/ddp093 doi


Carrier Proteins--genetics
Cell Respiration
Cells, Cultured
Child, Preschool
Electron Transport
Female
Fibroblasts--metabolism
Gene Expression
Heat-Shock Proteins--genetics
Humans
Infant
Male
Mitochondria--genetics
Mitochondrial Diseases--genetics
Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha
RNA-Binding Proteins
Transcription Factors--genetics
Up-Regulation