Skeletal muscle is a primary target of SOD1G93A-mediated toxicity.

Dobrowolny, Gabriella

Skeletal muscle is a primary target of SOD1G93A-mediated toxicity. [electronic resource] - Cell metabolism Nov 2008 - 425-36 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1932-7420

10.1016/j.cmet.2008.09.002 doi


Animals
Autophagy--physiology
Mice
Mice, Transgenic
Motor Neurons--metabolism
Muscle Contraction
Muscle, Skeletal--metabolism
Muscular Atrophy--metabolism
Mutation
Nerve Degeneration--pathology
Oxidative Stress
Reactive Oxygen Species--metabolism
Sarcolemma--pathology
Spinal Cord--pathology
Superoxide Dismutase--genetics
Superoxide Dismutase-1