Pristanic acid does not accumulate in peroxisomal acyl-CoA oxidase deficiency: evidence for a distinct peroxisomal pristanyl-CoA oxidase.

ten Brink, H J

Pristanic acid does not accumulate in peroxisomal acyl-CoA oxidase deficiency: evidence for a distinct peroxisomal pristanyl-CoA oxidase. [electronic resource] - Journal of inherited metabolic disease 1991 - 681-4 p. digital

Publication Type: Journal Article

0141-8955

10.1007/BF01799934 doi


Acyl-CoA Oxidase
Fatty Acids--metabolism
Humans
Microbodies--enzymology
Oxidation-Reduction
Oxidoreductases--deficiency
Phytanic Acid--blood