Cholesterol-deprivation increases mono-unsaturated very long-chain fatty acids in skin fibroblasts from patients with X-linked adrenoleukodystrophy.

Engelen, M

Cholesterol-deprivation increases mono-unsaturated very long-chain fatty acids in skin fibroblasts from patients with X-linked adrenoleukodystrophy. [electronic resource] - Biochimica et biophysica acta Mar 2008 - 105-11 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0006-3002

10.1016/j.bbalip.2007.12.003 doi


Adrenoleukodystrophy--metabolism
Cholesterol--deficiency
Fatty Acids, Monounsaturated--metabolism
Fibroblasts--enzymology
Gene Expression Regulation, Enzymologic
Humans
Oxidation-Reduction
Skin--enzymology
Stearoyl-CoA Desaturase--genetics