Severe endothelial dysfunction in the aorta of a mouse model of Fabry disease; partial prevention by N-butyldeoxynojirimycin treatment.

Heare, T

Severe endothelial dysfunction in the aorta of a mouse model of Fabry disease; partial prevention by N-butyldeoxynojirimycin treatment. [electronic resource] - Journal of inherited metabolic disease Feb 2007 - 79-87 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1573-2665

10.1007/s10545-006-0473-y doi


1-Deoxynojirimycin--analogs & derivatives
Animals
Aorta--drug effects
Disease Models, Animal
Enzyme Inhibitors--therapeutic use
Fabry Disease--drug therapy
Female
Humans
Male
Mice
Mice, Inbred C57BL
Mice, Knockout
Microscopy, Electron
Phenotype
alpha-Galactosidase--genetics