Lysosomal leukocyte beta-D-glucuronidase during enzyme replacement therapy in Fabry disease.

Goi, Giancarlo

Lysosomal leukocyte beta-D-glucuronidase during enzyme replacement therapy in Fabry disease. [electronic resource] - Biochimica et biophysica acta Sep 2005 - 300-6 p. digital

Publication Type: Comparative Study; Journal Article; Research Support, Non-U.S. Gov't

0006-3002

10.1016/j.bbadis.2005.05.002 doi


Adult
Analysis of Variance
Cytophotometry
Fabry Disease--drug therapy
Female
Glucuronidase--metabolism
Glycoside Hydrolases--blood
Humans
Leukocytes--enzymology
Lysosomes--enzymology
Male
Middle Aged
alpha-Galactosidase--therapeutic use