Immunoquantification and enzyme kinetics of alpha-L-iduronidase in cultured fibroblasts from normal controls and mucopolysaccharidosis type I patients.

Ashton, L J

Immunoquantification and enzyme kinetics of alpha-L-iduronidase in cultured fibroblasts from normal controls and mucopolysaccharidosis type I patients. [electronic resource] - American journal of human genetics Apr 1992 - 787-94 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0002-9297


Antibodies, Monoclonal
Cells, Cultured
Fibroblasts--enzymology
Humans
Iduronidase--analysis
Mucopolysaccharidosis I--enzymology