Amelioration of neutrophil membrane function underlies granulocyte-colony stimulating factor action in glycogen storage disease 1b.

Lesma, E

Amelioration of neutrophil membrane function underlies granulocyte-colony stimulating factor action in glycogen storage disease 1b. [electronic resource] - International journal of immunopathology and pharmacology - 297-307 p. digital

Publication Type: Clinical Trial; Journal Article; Research Support, Non-U.S. Gov't

0394-6320

10.1177/039463200501800212 doi


Actins--biosynthesis
Adolescent
Adult
Age Factors
Blood Glucose--analysis
Cell Membrane--enzymology
Child
Child, Preschool
Focal Adhesion Kinase 1
Focal Adhesion Protein-Tyrosine Kinases
Glycogen Storage Disease Type I--blood
Granulocyte Colony-Stimulating Factor--administration & dosage
Humans
Infant
Lactic Acid--analysis
Leukocyte Count
Neutropenia--blood
Neutrophils--cytology
Phosphorylation
Protein-Tyrosine Kinases--biosynthesis
Recombinant Proteins
Treatment Outcome