Trapping prion protein in the endoplasmic reticulum impairs PrPC maturation and prevents PrPSc accumulation.

Cardinale, Alessio

Trapping prion protein in the endoplasmic reticulum impairs PrPC maturation and prevents PrPSc accumulation. [electronic resource] - The Journal of biological chemistry Jan 2005 - 685-94 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0021-9258

10.1074/jbc.M407360200 doi


Animals
Biological Transport
Cell Line
Endoplasmic Reticulum--metabolism
Humans
Immunoglobulin Variable Region--immunology
Oligopeptides--metabolism
PrPC Proteins--immunology
PrPSc Proteins--immunology
Prion Diseases--metabolism
Protein Sorting Signals
Rats
Recombinant Proteins--metabolism