The lysosomal degradation of neuromedin B is dependent on tripeptidyl peptidase-I: evidence for the impairment of neuropeptide degradation in late-infantile neuronal ceroid lipofuscinosis.

Kopan, Sharmila

The lysosomal degradation of neuromedin B is dependent on tripeptidyl peptidase-I: evidence for the impairment of neuropeptide degradation in late-infantile neuronal ceroid lipofuscinosis. [electronic resource] - Biochemical and biophysical research communications Jun 2004 - 58-65 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

0006-291X

10.1016/j.bbrc.2004.04.142 doi


Aminopeptidases
Animals
Brain--metabolism
Cell Line
Cells, Cultured
Chromatography, High Pressure Liquid
Dipeptidyl-Peptidases and Tripeptidyl-Peptidases
Endopeptidases--chemistry
Fibroblasts--metabolism
Humans
Hydrogen-Ion Concentration
Lysosomes--metabolism
Magnetic Resonance Spectroscopy
Mice
Neurokinin B--analogs & derivatives
Neurons--metabolism
Peptide Hydrolases--metabolism
Peptides--chemistry
Protein Structure, Tertiary
Serine Proteases
Skin--metabolism
Time Factors
Tripeptidyl-Peptidase 1