Friedreich ataxia mouse models with progressive cerebellar and sensory ataxia reveal autophagic neurodegeneration in dorsal root ganglia.

Simon, Delphine

Friedreich ataxia mouse models with progressive cerebellar and sensory ataxia reveal autophagic neurodegeneration in dorsal root ganglia. [electronic resource] - The Journal of neuroscience : the official journal of the Society for Neuroscience Feb 2004 - 1987-95 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1529-2401

10.1523/JNEUROSCI.4549-03.2004 doi


Animals
Ataxia--etiology
Autophagy--genetics
Cerebellar Ataxia--etiology
Disease Models, Animal
Disease Progression
Friedreich Ataxia--complications
Ganglia, Spinal--pathology
Iron-Binding Proteins--genetics
Mice
Mice, Knockout
Mice, Neurologic Mutants
Motor Activity
Nerve Degeneration--genetics
Phenotype
Sensation Disorders--genetics
Frataxin