RNA-mediated neurodegeneration caused by the fragile X premutation rCGG repeats in Drosophila.

Jin, Peng

RNA-mediated neurodegeneration caused by the fragile X premutation rCGG repeats in Drosophila. [electronic resource] - Neuron Aug 2003 - 739-47 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.

0896-6273

10.1016/s0896-6273(03)00533-6 doi


Animals
Blotting, Western
Disease Models, Animal
Drosophila
Eye--pathology
Female
Fluorescent Antibody Technique
Fragile X Mental Retardation Protein
Fragile X Syndrome--genetics
HSP70 Heat-Shock Proteins--metabolism
Humans
Inclusion Bodies--metabolism
Male
Microscopy, Electron
Mutation
Nerve Degeneration--genetics
Nerve Tissue Proteins--genetics
Neurons--metabolism
RNA, Messenger--analysis
RNA-Binding Proteins
Reverse Transcriptase Polymerase Chain Reaction
Transgenes
Trinucleotide Repeat Expansion--genetics
Ubiquitin--metabolism