Enhanced expression of the alpha 7 beta 1 integrin reduces muscular dystrophy and restores viability in dystrophic mice.

Burkin, D J

Enhanced expression of the alpha 7 beta 1 integrin reduces muscular dystrophy and restores viability in dystrophic mice. [electronic resource] - The Journal of cell biology Mar 2001 - 1207-18 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't; Research Support, U.S. Gov't, P.H.S.

0021-9525

10.1083/jcb.152.6.1207 doi


Animals
Blotting, Western
Body Weight
Contracture--physiopathology
Creatine Kinase--genetics
Creatine Kinase, MM Form
Cytoskeletal Proteins--genetics
Dystrophin--genetics
Female
Hindlimb
Humans
Integrins--genetics
Isoenzymes--genetics
Joints
Kyphosis
Magnetic Resonance Imaging
Male
Membrane Proteins--genetics
Mice
Mice, Inbred mdx
Mice, Transgenic
Microscopy, Fluorescence
Muscle, Skeletal--pathology
Muscular Dystrophy, Animal--genetics
Muscular Dystrophy, Duchenne--genetics
Neuromuscular Junction--ultrastructure
Promoter Regions, Genetic
Rats
Receptors, Cholinergic--metabolism
Survival Rate
Transgenes
Utrophin