Evidence for a short-chain carnitine-acylcarnitine translocase in mitochondria specifically related to the metabolism of branched-chain amino acids.

Roe, D S

Evidence for a short-chain carnitine-acylcarnitine translocase in mitochondria specifically related to the metabolism of branched-chain amino acids. [electronic resource] - Molecular genetics and metabolism Jan 2000 - 69-75 p. digital

Publication Type: Journal Article; Research Support, Non-U.S. Gov't

1096-7192

10.1006/mgme.1999.2950 doi


Amino Acids, Branched-Chain--metabolism
Biological Transport
Carnitine--analogs & derivatives
Carnitine Acyltransferases--deficiency
Cells, Cultured
Child
Deuterium--metabolism
Fibroblasts--enzymology
Humans
Intracellular Membranes--metabolism
Isoleucine--metabolism
Mass Spectrometry
Metabolism, Inborn Errors--enzymology
Mitochondria--enzymology
Oxidation-Reduction