Survival, but not maturation, is affected in neutrophil progenitors from GSD-1b patients. [electronic resource]
Producer: 20120905Description: 287-300 p. digitalISSN:- 1573-2665
- Adolescent
- Animals
- Antiporters -- deficiency
- Apoptosis -- genetics
- Cell Differentiation -- genetics
- Child
- Child, Preschool
- Cytokines -- blood
- Female
- Glucose -- metabolism
- Glycogen Storage Disease Type I -- blood
- Hematopoietic Stem Cells -- metabolism
- Homeostasis -- genetics
- Humans
- Inflammatory Bowel Diseases -- blood
- Intestinal Mucosa -- metabolism
- Leukocytes, Mononuclear -- metabolism
- Male
- Mesenchymal Stem Cells -- metabolism
- Mice
- Mice, Inbred NOD
- Mice, SCID
- Monosaccharide Transport Proteins -- deficiency
- Neutropenia -- blood
- Neutrophils -- metabolism
- Survival Rate
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Publication Type: Journal Article; Research Support, Non-U.S. Gov't
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