Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway. [electronic resource]
Producer: 20120525Description: 5-12 p. digitalISSN:- 1573-2665
- Amino Acid Metabolism, Inborn Errors -- diagnosis
- Amino Acids, Branched-Chain -- metabolism
- Animals
- Enoyl-CoA Hydratase -- metabolism
- Humans
- Hydroxybutyrate Dehydrogenase -- metabolism
- Methylmalonate-Semialdehyde Dehydrogenase (Acylating) -- metabolism
- Mitochondria -- metabolism
- Models, Chemical
- Oxidoreductases Acting on CH-CH Group Donors -- metabolism
- Oxygen -- chemistry
- Thiolester Hydrolases -- metabolism
- Valine -- chemistry
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Publication Type: Journal Article
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