Regulatory insertion removal restores maturation, stability and function of DeltaF508 CFTR. [electronic resource]
Producer: 20100820Description: 194-210 p. digitalISSN:- 1089-8638
- Adenosine Triphosphate -- metabolism
- Animals
- Binding Sites -- genetics
- Biological Transport, Active
- Cell Line
- Cell Membrane -- metabolism
- Cricetinae
- Cystic Fibrosis -- genetics
- Cystic Fibrosis Transmembrane Conductance Regulator -- chemistry
- Humans
- In Vitro Techniques
- Mice
- Models, Molecular
- Molecular Dynamics Simulation
- Mutant Proteins -- chemistry
- Protein Interaction Domains and Motifs
- Protein Processing, Post-Translational
- Protein Stability
- Recombinant Proteins -- chemistry
- Sequence Deletion
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Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
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